A Primary Pulmonary Primitive Neuroectodermal Tumor Invading the Left Atrium Through the Right Inferior Pulmonary Vein: A Case Report and Literature Review
Abstract
Primitive neuroectodermal tumors (PNETs) are rare and aggressive, typically occurring in bones and soft tissues. This report describes a 12-year-old Chinese girl with primary pulmonary PNET invading the left atrium. She presented with right chest pain, shortness of breath, and dry cough for two months. Contrast-enhanced CT and PET-CT revealed a lung mass involving the left atrium. Transthoracic echocardiography showed a heterogeneous mass extending into the left atrium via the right inferior pulmonary vein. Needle biopsy diagnosed primary pulmonary PNET. Combination chemotherapy, monitored by echocardiography, reduced the tumor size, followed by surgical resection. Five years post-diagnosis, there was no recurrence.
Fields of Study & Subjects
Sarcoma Diagnosis and Treatment
Bone Tumor Diagnosis and Treatments
Oral and Craniofacial Lesions
Publication details
- Journal / source
- Journal of Clinical Ultrasound
- Volume
- 54
- Issue
- 5
- Pages
- 1275–1281
- Publication date
- 2 January 2026
- Language
- EN