A Case Series of Lymphangioleiomyomatosis, a Rare Cystic Lung Disease
Abstract
Lymphangioleiomyomatosis (LAM) is a rare interstitial lung disease that predominantly affects women of childbearing age. In this case series, we presented five cases diagnosed with LAM in our clinic in the last 2 years. All cases were female, and their ages ranged from 40 to 54 years. The primary symptoms of LAM seen in the cases were exertional dyspnea and cough. Radiological examination revealed multiple bilateral thin-walled air cysts on high-resolution computed tomography (HRCT) in all cases. In three cases, the diagnosis of LAM was made histopathologically by wedge resection. Awareness of this rare disease's clinical and radiological features is critical for early diagnosis and timely initiation of treatment.
Fields of Study & Subjects
Tuberous Sclerosis Complex Research
Medical Imaging and Pathology Studies
Interstitial Lung Diseases and Idiopathic Pulmonary Fibrosis
Publication details
- Journal / source
- Respirology Case Reports
- Volume
- 14
- Issue
- 3
- Pages
- e70535–e70535
- Publication date
- 1 March 2026
- Language
- EN