Pediatric triad of craniofacial fibrous dysplasia, Chiari malformation type I and syringomyelia: a case report
Abstract
Fibrous dysplasia is a benign bone disease characterized by the replacement of normal bone tissue with fibrous tissue, resulting in irregular bone structure. Cases of craniofacial fibrous dysplasia in children associated with Chiari type I malformation and syringomyelia are extremely rare. This case illustrates the complex clinical manifestations of craniofacial fibrous dysplasia along with Chiari type I malformation and syringomyelia, in which surgical intervention significantly improved the prognosis, and follow-up revealed near-complete resolution of the syringomyelia. It offers valuable insights for managing similar cases in the future.
Fields of Study & Subjects
Bone Tumor Diagnosis and Treatments
Soft tissue tumor case studies
Heterotopic Ossification and Related Conditions
Publication details
- Journal / source
- Acta Neurochirurgica
- Volume
- 168
- Issue
- 1
- Pages
- 2–2
- Publication date
- 3 January 2026
- Language
- EN