When Proteins Go MAD—Misfolded, Amplified, Detected: Advances in α-Synuclein Pathophysiology and RT-QuIC Detection

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Authors: Naďa Labajová, A. Polak, Ondrej Cehlár, Pavle Križan, Jozef Hritz, Martin Kolísek, Matěj Škorvánek, Rostislav Škrabana, Branislav Kováčech, Norbert Žilka
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References: 170

Abstract

Α-Synuclein (α-Syn) aggregation and fibrillation are pathological hallmarks of several neurodegenerative disorders, collectively termed synucleinopathies. The misfolded α-Syn protein exhibits a prion-like seeding behavior, promoting misfolding, intracellular spread, and progressive neurodegeneration. Recent advances in structural biology have revealed critical insights into the conformational heterogeneity of α-Syn aggregates and their strain-specific properties across distinct synucleinopathies. In parallel, significant progress has been made in biomarker development, particularly with the arrival of seed amplification assays. Among these, Real-Time Quaking-Induced Conversion (RT-QuIC) has emerged as a highly sensitive, specific, and scalable method for detecting pathogenic α-Syn species in cerebrospinal fluid and other tissues. This review summarizes the latest findings from structural studies on α-Syn oligomers and aggregates, their relevance to disease mechanisms, and highlights RT-QuIC as the most clinically advanced and rapidly evolving assay. We discuss its potential for early, biomarker-driven diagnostics, patient stratification, and clinical implementation.

Fields of Study & Subjects

Parkinson's Disease Mechanisms and Treatments Neurological disorders and treatments Genetic Neurodegenerative Diseases

Publication details

Journal / source
Molecular Neurobiology
Volume
63
Issue
1
Pages
352–352
Publication date
1 January 2026
Language
EN