Peripheral blood UBA1 variant burden predicts poor outcomes in VEXAS syndrome: a nationwide prospective study

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Authors: Yohei Kirino, Ayaka Maeda, Kana Higashitani, Nobuyuki Horita, Tomoyuki Asano, Kiyoshi Migita, Y. Motomura, Ryo Rokutanda, Daisuke Kobayashi, Masao Tamura, N. Kanazawa, Kazunori Furuhashi
+55 more Yasushi Kondo, Ken Nagahata, Hiroki Takahashi, H. Kobayashi, Shuhei Yao, Keiko Yamagami, Kaori Uchino, Yukiko Hidaka, Hiroaki Ida, Dai Kishida, Tomohito Sato, Kunihiro Ichinose, Takako Miyamae, Kohei Tsujimoto, Yuta Inoue, Yuichiro Fujieda, Koji Mishima, Tomohiro Tsuji, Kazuki Tanaka, Haruka Noda, Haruka Noda, Yuji Miyoshi, Naoto Yokogawa, Shinji Ota, Hirotake Sakuraba, Jumpei Nishi, Takuya Inoue, Sei Muraoka, Toshihiro Nanki, Toshimasa Shimizu, Tomohiro Koga, Yutaka Inaba, Masaki Matsubara, Kiyomi Yoshimoto, Anna Hasegawa, K. Ikeda, Rena Motohashi, Yoichi Takeuchi, Motoaki Shiratsuchi, Masayori Moriyama, Kentaro Noda, Shinichiro Saito, Hiroyuki Hagiyama, Tetsuya Honda, Reiko Kageyama, Norie Nakatani, Tatsunori Goto, Mitsumasa Kishimoto, Tomoya Watanabe, Yukie Yamaguchi, Ryuta Nishikomori, Osamu Ohara, Tatsuma Ban, Tomohiko Tamura, Hideaki Nakajima
Cited by: 2
References: 28

Fields of Study & Subjects

Otitis Media and Relapsing Polychondritis Osteomyelitis and Bone Disorders Research IgG4-Related and Inflammatory Diseases

Publication details

Journal / source
Annals of the Rheumatic Diseases
Publisher
Elsevier BV
Publication date
1 April 2026
Language
EN