External validation of the DSP-risk score for prediction of clinically significant ventricular arrhythmias in primary prevention patients with desmoplakin cardiomyopathy–associated genetic variants

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Authors: Alessio Gasperetti, Barbara Bauce, Alexandros Protonotarios, Brittney A. Murray, Crystal Tichnell, Marika Martini, Petros Syrris, Eric Smith, Matteo Dal Ferro, Alessia Paldino, Gianfranco Sinagra, Maria Iascone
+51 more Anna Maria Iorio, Roberta Scotto, Manuela Iseppi, Leonardo Calò, Cinzia Crescenzi, Marco Schiavone, Silvia Ravaro, Lia Crotti, Daniela Vargas, Paul Anders Sletten Olsen, Maddalena Graziosi, Elena Biagini, Giovanni Peretto, Stacey A. Peters, Alexandra Apostu, Ruxandra Jurcut, Sing Chien Yap, Ardan M. Saguner, Firat Duru, stefan zimmerman, Liang Tung Chen, Tiziana Felice, Claudia Raineri, Veronica Dusi, Lidia Carrillo-Mora, Eva Cabrera-Romero, Juan Ramon Gimeno, Carlos Fernández-Sellers, Esther Zorio, Michele Ciabatti, Vera Fico, Mattia Targetti, Maurizio Pieroni, Julia Cadrin-Tourigny, Victoria N. Parikh, Steven Muller, Anneline SJM te Riele, J. Peter van Tintelen, Moniek Cox, Adam Helms, Kristina Haugaa, Kalliopi Pilochou, Matthew Taylor, Luisa Mestroni, Perry Elliott, Marco Merlo, Elena Arbelo, Kathérine C. Wu, Cynthia A. James, Hugh Calkins, Richard T. Carrick
Cited by: 1
References: 26

Fields of Study & Subjects

Chemotherapy-induced cardiotoxicity and mitigation Cardiac electrophysiology and arrhythmias Cardiomyopathy and Myosin Studies

Publication details

Journal / source
Heart Rhythm
Publisher
Elsevier BV
Volume
23
Issue
10
Pages
e2585-e2594
Publication date
1 April 2026
Language
EN