Fibrillary glomerulonephritis: clinicopathological characteristics and treatment in a spanish tertiary center

Nefrología (English Edition) 2026 Open access

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Authors: Efrain Tatis, Natalia Ramos-Terrades, Alejandra Gabaldón, Irene Agraz, Marina López-Martínez, Sara Núñez-Delgado, Juan Carlos León-Román, Néstor Toapanta, Sheila Bermejo, Oriol Bestard, María José Soler
DOI: 10.1016/j.nefroe.2026.501417
Cited by: 0
References: 17

Abstract

INTRODUCTION: Fibrillary glomerulonephritis (FGN) has a poor prognosis and lacks standardized treatment. In this study, we describe clinicopathological characteristics, clinical course, and management of patients with FGN at our center. MATERIALS AND METHODS: A retrospective cohort study of 13 patients diagnosed with FGN by positive DNAJB9 at kidney biopsy between 2019 and 2024. Demographic data, comorbidities, laboratory values, histopathological findings, and treatments were collected, Complete remission was defined as proteinuria 50% reduction in proteinuria to

Fields of Study & Subjects

Renal Diseases and Glomerulopathies Vasculitis and related conditions Multiple Myeloma Research and Treatments

Publication details

Journal / source
Nefrología (English Edition)
Volume
46
Issue
2
Pages
501417–501417
Publication date
1 February 2026
Language
EN