Interventional, surgical, and clinical management of Abernethy malformations: A case series and novel anatomic variant
Abstract
Abernethy malformation is a rare congenital extrahepatic portosystemic shunt resulting from the persistence of embryonic vessels in the splanchnic venous system. There are 2 known types of Abernethy malformations: type I and II; both of which involve aberrant drainage of the portal venous blood into the inferior vena cava. Here, we detail the anatomy as well as clinical, surgical, and interventional management of 4 patients with Abernethy malformations. In addition, we detail a patient with a previously undescribed anatomic variant of the Abernethy type II malformation: a portosystemic shunt into an interrupted inferior vena cava in which central venous return was provided through the azygous/hemiazygos system.
Fields of Study & Subjects
Liver Disease and Transplantation
Congenital Heart Disease Studies
Organ Transplantation Techniques and Outcomes
Publication details
- Journal / source
- Radiology Case Reports
- Volume
- 21
- Issue
- 3
- Pages
- 1338–1345
- Publication date
- 5 January 2026
- Language
- EN