STING activation induces polarized cytokine secretion of IFN-β and IL-17A promoting photoreceptor death and choroidal disruption in age-related macular degeneration

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Authors: Chao Huang, Vishnu Suresh Babu, Sridhar Bammidi, Jakob Arnold, Martin Ebeling, Gabriella Widmer, Pamela Strassburger, Mirjana Lazendic, Sabine Grüner, Janis Koester, Puja Dutta, Stacey Hose
+12 more Sonali Singh, Pooja Gautam, Eleonora Maries Lad, Peter D. Westenskow, Oksana Kutsyr, Karl G. Csaky, Sayan Ghosh, Srinivas R. Sripathi, Alan D. Proia, Miguel Flores‐Bellver, Debasish Sinha, Derrick Feenstra
Cited by: 1
References: 89

Abstract

Age-related macular degeneration (AMD) represents one of the therapeutic challenges of aging eye diseases. Our investigation reveals the stimulator of interferon genes (STING) pathway as an orchestrator of immune-mediated retinal degeneration, exhibiting biphasic, stage-dependent functionality-providing cytoprotection in healthy tissue but driving pathogenic inflammation during early AMD progression. Through immunohistochemical analysis of human eyes, we demonstrate stage-dependent cytoplasmic STING upregulation with parallel IFN-β activation. Using patient-derived induced pluripotent stem cells-retinal pigment epithelium (iPSC-RPE) from AMD siblings, we discovered polarized cytokine secretion: apical IFN-β triggers photoreceptor apoptosis in human retinal organoids, while basal IL-17A compromises choroidal neovascularization. The Cryba1 conditional knockout (cKO) AMD-like mouse model confirms STING-driven IL-17A expression, while Il17a knock-in mice substantiate vascular alterations. STING activation establishes a pathogenic feed-forward loop between interferons and IL-17A. Single-cell transcriptomics following AAV2-mediated IFN-β overexpression reveals metabolic and phototransduction dysregulation. Both pharmacological STING inhibition with SN-011 and genetic approaches demonstrate therapeutic rescue. Cryba1/Sting double heterozygous (dhet) mice maintain homeostatic gene expression preserving retinal architecture and function. These findings establish STING as the master regulator simultaneously controlling multiple AMD pathologies through spatially organized inflammation, transforming from protective surveillance to pathogenic driver, and identifying a unified therapeutic target with demonstrated functional rescue across multiple experimental paradigms.

Fields of Study & Subjects

interferon and immune responses Ocular Diseases and Behçet’s Syndrome Retinal Diseases and Treatments

Publication details

Journal / source
Cell Death and Disease
Publisher
Springer Science and Business Media LLC
Volume
17
Issue
1
Publication date
27 February 2026
Language
EN