Taussig–Bing heart with pulmonary hypertension in a rare adult survivor: multimodality imaging insights

A 28-year-old man was admitted for exertional dyspnoea since childhood and an untreated congenital heart disease. Transthoracic echocardiography showed bidirectional low-velocity shunt dominated by right-to-left flow at the ventricular septal defect (VSD; Panel A). Computed tomography angiography revealed transposition of the great arteries, a subpulmonary 1.9 cm VSD (black asterisk), and markedly pulmonary hypertension with diameter of 4.7 cm (Panels B–E), confirming a Taussig–Bing syndrome. Cardiac magnetic resonance imaging confirmed the above cardiovascular abnormities and further demonstrated the presence of pulmonary regurgitation (flow void; Panels F and G). The Taussig–Bing heart, a rare and complex congenital heart malformation, is frequently associated with transposition of the great arteries, a disorder that significantly impact patients’ survival outcomes. Untreated patients rarely survive to adulthood. To our knowledge, the combination of Taussig–Bing with pulmonary hypertension has not been previously documented. Multimodality imaging allows comprehensive delineation of the intricate anatomical and haemodynamic derangement, providing critical guidance for potential intervention and long-term management.