Paediatric long QT syndrome: clinical outcomes and therapy in the Spanish National Registry

European Heart Journal 2026 Open access

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Authors: Francesca Perín, Antonio J. Cartón, Francisco José Bermúdez-Jiménez, Bárbara C. Fernández-Barrio, Roger Esmel-Vilomara, Laura Marcos-Fuentes, Fernando Rueda Nuñez, María del Mar Rodríguez Vázquez del Rey, Elena Montañés Delmás, Ariadna Ayerza Casas, Belén Fernández-Tudela, María Teresa Viadero
+23 more Francisco José Castro-García, Ana Siles, Enrique Blanca-Jover, Laura Caravaca-Pantoja, Andrea Bueno-Gómez, Beatriz Salamanca-Zarzuela, Paula de Vera McMullan, Gloria López-Blanco, Beatriz Plata Izquierdo, Soledad Jimenez Casso, María Isabel Robles, Miguel Ángel Matamala Morillo, Laura del Rey Megias, Sandra Rocamora Salort, Carlota Aparicio Fernández de Gatta, Marta Villares Alonso, María Arroyas, Ángeles Ortega Montes, Andrea Greco, Estefanía Martinez-Barrios, Juan Jiménez‐Jáimez, Ferran Rosés‐Noguer, Georgia Sarquella‐Brugada
DOI: 10.1093/eurheartj/ehag513
Cited by: 1
References: 45

Abstract

BACKGROUND AND AIMS: Congenital long QT syndrome (LQTS) is a heterogeneous disorder in which genotype and QTc duration modulate the risk of major arrhythmic events (MAEs), but contemporary paediatric outcome data remain limited. This study aimed to characterize clinical features, management strategies, and predictors of MAEs in a nationwide paediatric LQTS cohort. METHODS: This retrospective multicentre study analysed children (

Fields of Study & Subjects

Cardiac electrophysiology and arrhythmias Receptor Mechanisms and Signaling ECG Monitoring and Analysis

Publication details

Journal / source
European Heart Journal
Publisher
Oxford University Press (OUP)
Publication date
17 July 2026
Language
EN