First presentation of idiopathic granulomatosis with polyangiitis in an adolescent
Abstract
This case report demonstrates a paediatric patient with antineutrophil cytoplasmic antibody-associated vasculitis, most consistent with a diagnosis of granulomatosis with polyangiitis (GPA), who presented with extensive airway involvement. It highlights that, although rare, the potential occurrence of GPA can be clinically challenging.
Fields of Study & Subjects
Vasculitis and related conditions
Autoimmune and Inflammatory Disorders
Otitis Media and Relapsing Polychondritis
Publication details
- Journal / source
- BMJ Case Reports
- Volume
- 19
- Issue
- 2
- Pages
- e266449–e266449
- Publication date
- 1 February 2026
- Language
- EN