Inflammation and mucus properties in inherited diseases of mucociliary clearance

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Authors: Amelia Shoemark
Cited by: 1
References: 14

Abstract

Extract Primary ciliary dyskinesia (PCD) and cystic fibrosis (CF) are inherited disorders of mucociliary clearance that lead to persistent lifelong productive cough, frequent exacerbations and, ultimately, bronchiectasis [1, 2].

Fields of Study & Subjects

Cystic Fibrosis Research Advances Respiratory and Cough-Related Research Interstitial Lung Diseases and Idiopathic Pulmonary Fibrosis

Publication details

Journal / source
European Respiratory Journal
Publisher
European Respiratory Society (ERS)
Volume
67
Issue
2
Pages
2502426–2502426
Publication date
1 February 2026
Language
EN