Inflammation and mucus properties in inherited diseases of mucociliary clearance
Abstract
Extract Primary ciliary dyskinesia (PCD) and cystic fibrosis (CF) are inherited disorders of mucociliary clearance that lead to persistent lifelong productive cough, frequent exacerbations and, ultimately, bronchiectasis [1, 2].
Fields of Study & Subjects
Cystic Fibrosis Research Advances
Respiratory and Cough-Related Research
Interstitial Lung Diseases and Idiopathic Pulmonary Fibrosis
Publication details
- Journal / source
- European Respiratory Journal
- Publisher
- European Respiratory Society (ERS)
- Volume
- 67
- Issue
- 2
- Pages
- 2502426–2502426
- Publication date
- 1 February 2026
- Language
- EN