Cystic Biliary Atresia Combined with Gallbladder Duplication: A Case Report

Abstract Congenital biliary atresia (BA) is a disease involving obstruction of both intrahepatic and extrahepatic bile ducts, leading to cholestatic liver disease, progressive hepatic fibrosis and eventual liver failure. A specific subtype, cystic biliary atresia (CBA), is characterized by the presence of a cyst near the porta hepatis or in the proximal extrahepatic duct. However, as this cyst does not communicate with the intrahepatic biliary tree, it fails to alleviate progressive bile stasis and hepatic fibrosis. Additionally, gallbladder duplication is a rare biliary malformation where an accessory gallbladder is situated adjacent to or connected with the primary one. Notably, the cooccurrence of neonatal CBA and gallbladder duplication is exceedingly rare. To our knowledge, no similar literature has been reported.