Unraveling GDAP1: Bridging Mitochondrial Biology and Peripheral Neuropathy

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Authors: Lara Cantarero, Janet Hoenicka, Francesc Palau
Cited by: 1
References: 106

Abstract

The mitochondrial outer membrane (OMM) plays a crucial role in maintaining cellular homeostasis by regulating mitochondrial dynamics, organelle interactions, and stress responses. In peripheral neurons-cells with high metabolic demands and long axons-the OMM acts as a vital platform for coordinating bioenergetics, calcium signaling, and redox balance. Ganglioside-induced differentiation-associated protein 1 (GDAP1), an OMM-anchored protein, has emerged as a key regulator of mitochondrial fission and transport, redox homeostasis, and mitochondrial membrane contact sites (MCSs). Genetic variants in GDAP1 cause Charcot-Marie-Tooth disease (CMT), emphasizing its essential role in peripheral nerve function. This review highlights the multifaceted functions of GDAP1 in neuronal physiology and as a model protein that integrates organelle communication and mitochondrial biology. We further discuss how GDAP1 dysfunction leads to structural and functional impairments in peripheral neurons, proposing the OMM and its microenvironment as critical targets for therapeutic intervention in inherited neuropathies.

Fields of Study & Subjects

Hereditary Neurological Disorders Mitochondrial Function and Pathology Neurological diseases and metabolism

Publication details

Journal / source
Biomolecules
Publisher
MDPI AG
Volume
16
Issue
2
Pages
280–280
Publication date
10 February 2026
Language
EN