Condroma de septum nasal: reporte de caso

Introduction: Enchondromatosis is a rare condition characterized by dyschondro­plastic lesions that predominantly affect long bones. Its involvement of the nasal cavity and paranasal sinuses is exceptional and poorly documented. Case report: A male patient with a history of enchondromatosis is described, in whom, during the evaluation of periorbital cellulitis, a heterogeneous lesion was incidentally identified in the left nasal cavity obstructing the osteomeatal complex. Surgical resection was performed, and histopathology confirmed an osteochondroma. Discussion: Nasal and paranasal involvement in enchondromatosis is rare and may present nonspecific symptoms or as an incidental finding. Diagnostic imaging is essential for lesion cha­racterization, and surgical resection remains the treatment of choice, given that these lesions do not respond to adjuvant therapies. Conclusion: Although enchondromato­sis typically affects long bones, its nasosinusal presentation should be considered in patients with this condition to guide appropriate management.