A rare case of midaortic syndrome: Vascular Behçet’s disease or Takayasu arteritis?

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Authors: Zeynep Ece Demirbaş, Abdullah Kemal TUYGUN
Cited by: 0

Abstract

This case report describes a 44-year-old man with midaortic syndrome and resistant hypertension, presenting a diagnostic challenge due to overlapping features of Behçet's disease and Takayasu arteritis. Imaging studies revealed severe aortic stenosis accompanied by aortic wall thickening, findings typically associated with Takayasu arteritis; however, the patient's clinical history and a positive pathergy test supported a diagnosis of Behçet's disease. Immunosuppressive therapy led to symptomatic improvement, and surgical management with thoracic endovascular aortic repair was successfully performed to address the aortic stenosis. This report discusses the possibility of Behçet's disease presenting with aortic stenosis-a rare vascular complication-or the coexistence of Behçet's disease and Takayasu arteritis.

Fields of Study & Subjects

Vasculitis and related conditions Ocular Diseases and Behçet’s Syndrome Infectious Aortic and Vascular Conditions

Publication details

Journal / source
Turkish Journal of Thoracic and Cardiovascular Surgery
Volume
34
Issue
2
Pages
172–174
Publication date
6 February 2026
Language
EN