Pulmonary Artery Morphology on Computed Tomography and Cardiac Catheterization in Congenital Heart Disease Patients with Pulmonary Stenosis and Atresia at Cho Ray Hospital

Abstract: Pulmonary stenosis and pulmonary atresia are complex congenital heart defects with high variability in clinical presentation and pulmonary artery anatomy. Research objective: To survey clinical and paraclinical characteristics, imaging characteristics of the pulmonary artery trunk and branches, and collateral circulation in patients with pulmonary artery stenosis and agenesis. Methods: This retrospective descriptive study was conducted at the Pediatric Cardiac Surgery Intensive Care Unit, Cho Ray Hospital, from March 2017 to August 2023. Results: Twenty-eight patients were evaluated, with a mean age of 5.13 ± 5.0 years. The most common symptoms were dyspnea (82%) and cyanosis (71%). On CT, pulmonary valve atresia was observed in 53.6% of cases, and 67.9% had no MAPCAs. Pulmonary artery confluence was present in 96.4% of cases. Among the 7 catheterizations performed, 57% revealed absence of the main pulmonary artery. Conclusion: CT and cardiac catheterization are essential for comprehensive evaluation of pulmonary circulation anatomy in patients with pulmonary stenosis and atresia, providing critical information for treatment planning and improving surgical outcomes