Rowell Syndrome with Lupus Podocytopathy: A Diagnostic Challenge

Rowell syndrome is a distinct subtype of systemic lupus erythematosus presenting with features of lupus as well as erythema multiforme. It has been well characterized by a different set of systemic signs and symptoms and a unique serological profile. Lupus podocytopathy (LP) is a rare pattern of lupus nephritis with a slightly different clinical and serological profile, natural course of the disease, as well as prognosis. A case of Rowell syndrome is presented, which was later diagnosed with LP on the basis of global effacement of podocytes on electron microscopy Cite this article as: Gera V, Kashif AW, Koshy V, et al. Rowell syndrome with lupus podocytopathy: A diagnostic challenge. Eur J Rheumatol. 2026, 13(1), 0007, doi:10.5152/eurjrheum.2026.25007.