How is congenital TTP complicated by secondary HLH managed?

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Authors: Tripdatabase
Cited by: 0

Abstract

Management of congenital TTP complicated by secondary HLH generally involves a combination of plasma exchange for TTP and standard HLH protocols, though direct evidence is sparse.

Fields of Study & Subjects

Complement system in diseases Autoimmune and Inflammatory Disorders Research Immunodeficiency and Autoimmune Disorders

Publication details

Journal / source
Zenodo (CERN European Organization for Nuclear Research)
Publication date
29 January 2026