What are the common peripheral muscle abnormalities observed in patients with cystic fibrosis and what are their etiologies?
Abstract
Patients with cystic fibrosis commonly experience peripheral muscle weakening and atrophy due to CFTR deficiency and associated nutritional, inflammatory, and lifestyle factors.
Fields of Study & Subjects
Cystic Fibrosis Research Advances
Muscle Physiology and Disorders
Nutrition and Health in Aging
Publication details
- Journal / source
- Zenodo (CERN European Organization for Nuclear Research)
- Publication date
- 14 February 2026
- Language
- EN