Isolated Unilateral Absence of Pulmonary Artery in an Adult

Unilateral absence of pulmonary artery (UAPA) is an uncommon condition with a prevalence of 1 in 200,000 young adults, which is characterised by congenital absence of either the left or right pulmonary artery and may be associated with or without other cardiac diseases. While the UAPA declares itself in infancy when associated with other congenital anomalies, patients with isolated UAPA usually remain asymptomatic and present in adulthood with symptoms such as dyspnoea, haemoptysis, recurrent infections, etc. We encountered an adult male patient who presented with haemoptysis and was diagnosed on further examination to have an absent right pulmonary artery. Considering the rarity and non-specific presentation of isolated UAPA, this case is being reported.