A Rare Association of a Cor Triatriatum Sinistrum and a Right Partial Anomalous Pulmonary Venous Return : A Route to Understanding the Disease

Abstract: A 56 day-old baby girl referred for recurrent respiratory tract infections and stridor , showed a rare association of a Cor riatriatum Sinister (CTS) and a right Partial Anomalous Pulmonary V enous Return (P APVR), in the form of a stenosed Scimitar vein, d r a i n i n g t h e r i g h t p u l m o n a r y v e i n s t o t h e sub dia phr agm ati c inf eri or ven a cav a (IV C), on echography and angiography . The baby underwent successful surgical repair of the CTS, by resection of the obstructive membrane and reconnection of the Scimitar vein to the left atrium. At the age of 5 years, the child is doing well without any evidence of obstruction on the right or the left pulmonary venous drainage.