Neuraxial Anesthesia in a Parturient With Newly Diagnosed Klippel-Trenaunay Syndrome: A Case Report

Klippel-Trenaunay syndrome (KTS) is a complex, congenital vascular disorder characterized by three primary manifestations: cutaneous capillary malformation (most commonly port-wine stain), congenital varicose veins, and soft tissue and bone hypertrophy. In the obstetric population, the evaluation of these vascular malformations is essential to mitigate bleeding risk with regional, neuraxial, and general anesthesia, particularly if there is the involvement of the spinal column or oropharyngeal airway. We report a unique case highlighting the successful administration of neuraxial anesthesia in a parturient with KTS undergoing an emergent cesarean section for fetal deterioration. In the absence of available imaging, careful consideration was given to balance the risks of neuraxial hematoma and a potentially difficult airway.