Rare Case of Multifocal Spinal Hemangioblastomas With Holocord Syringo-Hydromyelia in an Adolescent Male

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Authors: Rishi Meswani, Prashant Madhukar Onkar, SURESH VASANT PHATAK, Kajal Ramendranath Mitra, MAYANK RANGARI
Cited by: 0
References: 6

Abstract

Hemangioblastomas are benign, highly vascular tumors of the central nervous system. Although they most commonly arise in the cerebellum, they may also involve the brainstem and spinal cord. The presence of multiple spinal hemangioblastomas is frequently associated with von Hippel-Lindau (VHL) syndrome; however, sporadic cases without an underlying genetic syndrome can occur. Characteristic imaging features include avid post-contrast enhancement, associated syrinx formation, and intratumoral or peritumoral flow voids. Spinal hemangioblastomas account for a small proportion of intramedullary spinal tumors and are rarely reported in adolescents. We present a rare case of multifocal spinal hemangioblastomas with extensive holocord syringo-hydromyelia in an adolescent male patient without any evidence of VHL syndrome.

Fields of Study & Subjects

Ear and Head Tumors Vascular Malformations and Hemangiomas Spinal Dysraphism and Malformations

Publication details

Journal / source
Cureus
Volume
18
Issue
1
Pages
e102651–e102651
Publication date
30 January 2026
Language
EN